ARRHYTHMOGENIC RIGHT-VENTRICULAR DYSPLASIA - THERAPEUTIC OPTIONS DURING A 12 YEARS FOLLOW-UP OF ONE PATIENT

The replacement of muscle by fibrous and adipose tissue lead to arrhyt hmogenic right ventricular dysplasia. We report the clinical features and therapeutic options of a 50 years old male with the disease follow ed during 12 years. The latter included pharmacological therapy surgic al pseudoaneulysmal resection and radiofrequelzcy fulguration of a sec ond arrhythmogenic focus that appeared 10 after the surgical procedure . The patient remained asymptomatic after each therapy until the disea se progressed again. This follow up is one of the longest reported and documents the disease's clinical presentation evolution and treatment .