TRILATERAL RETINOBLASTOMA WITH SUPRASELLAR INVOLVEMENT

''Trilateral retinoblastoma'' (TRB) is the association of a midline in tracranial tumor with familial bilateral retinoblastoma. Classically, the intracranial tumor is a pineal region tumor (pineoblastoma) with h istology similar to retinoblastoma. We present a 7-month-old child wit h bilateral orbital retinoblastoma with a third tumor arising in the c hiasmatic cistern. The presentation and prognosis of patients with thi s association differ from those children with ''classical'' TRB. The p resentation, treatment, and outcome are described, with a review of th e literature.