F. Pombo et al., AORTIC CALCIFICATION AND RENAL CYSTS DEMONSTRATED BY CT IN A TEENAGERWITH ALAGILLE SYNDROME, Pediatric radiology, 25(4), 1995, pp. 314-315
Citations number
10
Categorie Soggetti
Radiology,Nuclear Medicine & Medical Imaging",Pediatrics
Alagille syndrome, or arteriohepatic dysplasia, is a disorder characte
rized by paucity of intrahepatic bile ducts, peculiar facies and skele
tal anomalies. We report a typical case of this syndrome in an 18-year
-old girl, in whom abdominal CIT showed bilateral renal cysts and aort
ic wall calcification, findings unreported in the radiological literat
ure.