MITRAL-VALVE PROLAPSE CAUSING SEVERE MITRAL REGURGITATION IN A PATIENT WITH ABSENT RIGHT PULMONARY-ARTERY

A 33-year-old man was investigated for dyspnea on exertion and the pre sence of a pansystolic murmur. Physical examination revealed dextrocar dia confirmed by chest radiograph, which also showed oligemic right lu ng field. Subsequent cardiac catheterization revealed secundum atrial septal defect, persistent left sided superior vena cava, and severe mi tral valve prolapse causing severe mitral regurgitation with pulmonary hypertension. The right pulmonary artery was absent. It is the first report of the association between severe mitral valve prolapse and abs ent right pulmonary artery.