A 41-year-old man presented with intermittent diplopia. Examination re
vealed mild, left sixth nerve palsy. MRI scan revealed a tumor involvi
ng the sphenoid sinus, clivus and cavernous sinus. Transphenoidal expl
oration and biopsy of the tumor was performed, and histology demonstra
ted malignant melanoma. Despite resection and radiation therapy, the p
atient died nine months later. An extensive blue nevus was present on
the left side of his scalp, and on surgical exploration this extended
intracranially as far as was explored. The histology of the brain lesi
on and the blue nevus were remarkably similar although cytologically,
the brain lesion was more atypical. It was concluded that the brain le
sion represented a metastasis or intracranial involvement from the blu
e nevus. Malignant blue nevus has been previously reported. This case
is important because it draws attention to the possibility that extens
ive lesions involving the scalp may have intracranial involvement and
may warrant aggressive management.