Sebaceous carcinoma is a rare, aggressive, malignant tumor derived fro
m the adnexal epithelium of sebaceous glands. It may arise in ocular o
r extraocular sites and exhibits such a variety of histologic growth p
atterns and diverse clinical presentations that the diagnosis is often
delayed for months to years. We discuss incidence as well as clinical
, histologic, diagnostic, prognostic, and management issues of this ag
gressive neoplasm.