IMPERFORATE ANUS, MALROTATION AND HIRSCHSPRUNGS-DISEASE - A RARE ASSOCIATION

The association of imperforate anus with anomalies of rectal innervati on is very rare. Moreover, malrotation only rarely accompanies these m alformations. We report 2 patients with this unusual triple associatio n and its impact on their management. Retrospectively both patients pr esented at birth with the same radiological picture of distended dista l colon and right-sided small bowel location. We discuss the importanc e of a systematic search for associated intestinal malformations in ca ses of imperforate anus in oder to avoid serious complications and to choose the optimal operative strategy.