CAROLIS-DISEASE COMPLICATING PREGNANCY

We describe two pregnancies in the same patient with Caroli's disease (congenital dilation of the intrahepatic bile ducts). The first pregna ncy was uneventful concerning the maternal Caroli's disease. The secon d pregnancy highlights the serious and potentially lethal complication s of an acute episode to both the fetus and mother. The patient had ac ute ascending cholangitis, disseminated intravascular coagulopathy, an d septic shock. Fetal distress necessitated delivery by cesarean secti on. The mother's postoperative course required prolonged critical care and interdisciplinary consultation. Both mother and neonate survived. We present the first report of Caroli's disease in pregnancy and revi ew implications to the pregnant patient.