DIARRHEA-ASSOCIATED HEMOLYTIC-UREMIC SYNDROME IN A CHILD WITH NAIL-PATELLA SYNDROME

A 5-year-old girl with nail-patella syndrome had diarrhea-associated h emolytic-uremic Syndrome. Nail-patella syndrome is associated with a g lomerulopathy characterized by the presence of fibrillar collagen with in the glomerular basement membrane. Hemolytic-uremic syndrome has als o been reported in patients with collagen type III glomerulopathy, a d isorder also characterized by the presence of fibrillar collagen withi n the basement membrane. Patients with nail-patella syndrome or with c ollagen type III glomerulopathy may be predisposed to hemolytic-uremic syndrome.