Spinal dural arteriovenous fistulas (SDAVFs) are the most common type
of spinal vascular malformation. The arteriovenous shunts, located ent
irely outside the spinal cord, cause a clinical picture of chronic pro
gressive myelopathy believed to arise from the effects of increased ve
nous pressure and impaired venous drainage on the spinal cord. Despite
their well-described clinical and angiographic features, no reports h
ave documented the spinal cord pathology in a case of angiographically
or pathologically proven SDAVF. We report such a patient in whom a sp
inal cord biopsy supported increased venous pressure as a mechanism of
neurologic dysfunction.