PRIMARY ADRENAL LYMPHOMA ASSOCIATED WITH ADRENAL INSUFFICIENCY - A DISTINCT CLINICAL ENTITY

We describe a case of a 42 year old male who presented with Addison's disease resulting from primary lymphoma of the adrenals. Our case and a review of the literature indicates that this distinct entity has som e unique clinical and radiologic features. In this entity, the lymphom a tends to be extranodal and have a poor prognosis. In addition, the c omputed tomography (CT) images have the unique appearance of enlargeme nt of the adrenal gland with maintenance of the adreniform shape. We s uggest that primary adrenal lymphoma is a distinct clinical entity and should be considered in patients with an elevated serum lactate dehyd rogenase, characteristic CT findings and Addison's disease.