THE HAIR COLLAR SIGN - MARKER FOR CRANIAL DYSRAPHISM

Citation
Ba. Drolet et al., THE HAIR COLLAR SIGN - MARKER FOR CRANIAL DYSRAPHISM, Pediatrics, 96(2), 1995, pp. 309-313
Citations number
20
Categorie Soggetti
Pediatrics
Journal title
ISSN journal
00314005
Volume
96
Issue
2
Year of publication
1995
Part
1
Pages
309 - 313
Database
ISI
SICI code
0031-4005(1995)96:2<309:THCS-M>2.0.ZU;2-Z
Abstract
Objective. To call attention to a cutaneous marker for neural tube clo sure defects of the scalp, the ''hair collar'' sign. This finding cons ists of a ring of long, dark, coarse hair surrounding a midline scalp nodule. Methods and Results. Four children with small congenital scalp nodules and the hair collar sign were studied from the standpoint of clinical findings, radiologic scans, and histology of the excised nodu les. All four had an overlying vascular stain in addition to the hair collar. Patients 1 and 2 were found to have encephaloceles, and one ha d heterotopic brain tissue. The fourth family refused surgery, but the clinical and radiologic findings were consistent with a diagnosis of atretic encephalocele. One infant had agenesis of the corpus callosum and a Dandy-Walker malformation as associated findings. Conclusions. T he ''hair collar'' sign should alert the pediatrician to the possibili ty of ectopic neural tissue in the scalp and/or underlying central ner vous system malformations.