SPINAL-ANESTHESIA IN A PATIENT WITH FRIEDREICHS-DISEASE

Friedreich's disease is a very rare neurological disorder that causes degeneration of the posterior roots of the spinal nerves and progresse s to the anterior roots, even in young adults. Hospital emergency team s face the question of choice of anaesthesia in such patients should g eneral anaesthesia be preferred to regional anaesthesia. We report a 3 6-year-old patient with spinocerebellar heredoataxia (Friedreich's dis ease) who underwent a proctological procedure after administration of spinal anaesthesia with 3 mg hyperbaric bupivacaine in a sitting posit ion. Both the intra-and post-operative courses were unremarkable; in p articular, with regard to the underlying neurological disease, no comp lications were observed.