SUCCESSFUL PREGNANCY FOLLOWING GONADOTROPIN THERAPY IN A YOUNG FEMALEWITH JUVENILE IDIOPATHIC HEMOCHROMATOSIS AND SECONDARY HYPOGONADOTROPIC HYPOGONADISM

Heart failure and hypogonadotropic hypogonadism are the most frequent clinical problems encountered in patients with juvenile idiopathic hem ochromatosis (JIH). In this context, amenorrhea is one of the first sy mptoms in female patients, and hormone therapy must be added to phlebo tomy to restore menstrual cycles. Here we report the case of a woman i n childbearing age with hypogonadotropic hypogonadism due to JIH. Foll owing therapy with gonadotropinic hormones the patient had a twin preg nancy with term delivery. The newborns presented a normal iron status. This confirms that early diagnosis and treatment of JIH are important to prevent irreversible organ damage and shows that the female reprod uctive function can be preserved in adequately treated patients.