We studied seven consecutive patients who experienced amaurosis as a p
rominent feature of their seizures. The mean age of seizure onset was
4 years. Six patients had MRI abnormalities including ischemic, trauma
tic, and space-occupying lesions, with five limited to the parietal-oc
cipital region. Six patients had unilateral, posterior interictal spik
e and slow wave complexes. Four patients experienced severe postictal
headache and nausea. Absence of a family history of seizures distingui
shed the patients with MRI lesions from previously presented series of
benign occipital lobe epilepsy. We conclude that the constellation of
ictal amaurosis, occipital paroxysms, and postictal migrainous sympto
ms does not necessarily signify a benign, nonlesional epilepsy; MRI is
recommended for such patients without a family history of similar sei
zures.