THE SHOULDER AND ELBOW IN APERTS-SYNDROME

Nine children with Apert's syndrome were studied and found to have pro gressive bony dysplasia in the shoulder and elbow. The children showed loss of joint motion and radiographic abnormalities including subluxa tion and flattening of the humeral head with irregularities of the gle noid. The elbow showed flattening and subluxation of the radial head i n radiographs and a positive click on physical examination. The limita tion of motion and the presence of bony defects were progressive, sugg esting that Apert's syndrome is a progressive generalized dysplasia.