ATHYMORRHOEA AND PROGRESSIVE PARAPLEGIA R EVEALING ADRENOLEUKOMYELONEUROPATHY IN AN ADULT

Citation
C. Brosset et al., ATHYMORRHOEA AND PROGRESSIVE PARAPLEGIA R EVEALING ADRENOLEUKOMYELONEUROPATHY IN AN ADULT, Revue neurologique, 151(6-7), 1995, pp. 388-391
Citations number
7
Categorie Soggetti
Clinical Neurology
Journal title
ISSN journal
00353787
Volume
151
Issue
6-7
Year of publication
1995
Pages
388 - 391
Database
ISI
SICI code
0035-3787(1995)151:6-7<388:AAPPRE>2.0.ZU;2-I
Abstract
A 40-year-old man presented with both paraparesia and an athymhormic S yndrome. Bicapsular lesions together with abnormal evoked,motor potent ials suggested cortical and spinal involvement in the deficiency syndr ome. The neuropsychologic symptoms appeared to be secondary to bilater al pallidium lesions. Associated signs,were adrenoleukocystrophy and a drenomyeloneuropathy, suggesting the term, adrenoleukocyeloneuropathy.