C. Brosset et al., ATHYMORRHOEA AND PROGRESSIVE PARAPLEGIA R EVEALING ADRENOLEUKOMYELONEUROPATHY IN AN ADULT, Revue neurologique, 151(6-7), 1995, pp. 388-391
A 40-year-old man presented with both paraparesia and an athymhormic S
yndrome. Bicapsular lesions together with abnormal evoked,motor potent
ials suggested cortical and spinal involvement in the deficiency syndr
ome. The neuropsychologic symptoms appeared to be secondary to bilater
al pallidium lesions. Associated signs,were adrenoleukocystrophy and a
drenomyeloneuropathy, suggesting the term, adrenoleukocyeloneuropathy.