SINUS HISTIOCYTOSIS WITH MASSIVE LYMPHADENOPATHY (ROSAI-DORFMAN DISEASE) - REPORT OF A PATIENT WITH ISOLATED RENOTESTICULAR INVOLVEMENT AFTER CURE OF NON-HODGKINS-LYMPHOMA

Sinus histiocytosis with massive lymphadenopathy (SHML) - Rosai-Dorfma n disease - is a rare but well-defined benign histiocytic proliferativ e disorder. We report an unusual patient, cured of non-Hodgkin's lymph oma, who presented 12 years later with renotesticular SHML associated with IgA monoclonal gammopathy, but without any evidence of relapsed l ymphoma. The genitourinary manifestations of this disorder with massiv e lymphadenopathy and its rare association with malignant lymphoma are reviewed.