Intraocular malignant mesenchymal tumors are very rare, and only a few
case reports of such primary and metastatic tumors have been reported
. We report a case of a malignant mesenchymoma involving the entire uv
eal tract. A 21-year-old woman presented with a tumor on the whole iri
s of the right eye, which caused intractable glaucoma. Upon enucleatio
n of the eye, a very anaplastic tumor was found to occupy the whole uv
eal tract; its features were compatible with a tumor of mesenchymal or
igin, including rhabdomyosarcomatous and liposarcomatous characteristi
cs. Choroidal osteoma was a coincidental finding. The histologic findi
ngs of the tumor were of two types of malignant mesenchymal tumors, an
d therefore the diagnosis of malignant mesenchymoma was made. This is
to our knowledge the first tumor of its kind to be reported intraocula
rly.