RECURRENT INFLAMMATION IN INCONTINENTIA PIGMENTI OF A 7-YEAR-OLD CHILD

A young girl has undergone the typical skin manifestations of incontin entia pigmenti, leaving now only discrete hyperpigmentation on the fle xor sides of the lower extremities. Each time when she has a feverish infection, a recurrence of inflammation can be seen within the hyperpi gmented areas. At the same time when the fever subsides, the acute ski n manifestations disappear as well. The combination of recurrent infla mmatory skin manifestations within the hyperpigmented skin areas of in continentia pigmenti and fever is unique. The reasons for this phenome non and for its strict limitation to the areas of incontinentia pigmen ti remain unclear.