H. Jonsson et T. Ivert, SURVIVAL CLINICAL-RESULTS UP TO 26 YEARS AFTER AND REPAIR OF TETRALOGY OF FALLOT, Scandinavian journal of thoracic and cardiovascular surgery, 29(2), 1995, pp. 43-51
Repair of tetralogy of Fallot was performed on 165 patients (median ag
e 7 years, range 4 months-54 years) in 1966-1976. The 30-day mortality
rate was 15%. High postrepair right ventricular/left ventricular pres
sure ratio (P-RV/LV) was a predictor of early mortality. Complete atri
oventricular block of varying duration, though associated with 42% of
the early deaths, was not an independent risk factor in multivariate a
nalysis. The 20-year survival rate (excluding early deaths) was 84%. R
eoperation was done in ten patients. Of the 16 late deaths, eight were
sudden. Old age at repair and use of transannular patch correlated wi
th risk of late death. Complete atrioventricular block, acyanosis, yea
r of surgery, sex and P-RV/LV did not significantly influence long-ter
m survival. Follow-up (median 19, range 13-26, years) comprised 110 su
rvivors, 95% of whom were asymptomatic, 77% in employment, 65% had par
ticipated in school athletics and 58% regularly exercised, but 40% did
not have regular medical examinations. Operation at age 3-5 years had
the most favourable prognosis.