Ao. Ciccarelli et al., PLASTIC AND RECONSTRUCTIVE SURGERY IN EPIDERMOLYSIS-BULLOSA - CLINICAL-EXPERIENCE WITH 110 PROCEDURES IN 25 PATIENTS, Annals of plastic surgery, 35(3), 1995, pp. 254-261
We present clinical experience with 110 reconstructive procedures in 2
5 patients with epidermolysis bullosa, a group of rare heritable disor
ders characterized by marked fragility of the skin and mucosa. We disc
uss management of hand and foot deformities unique to epidermolysis bu
llosa patients, excision of squamous cell carcinoma, and reconstructio
n of oral, nasal, and ocular tissues. All patients underwent these pro
cedures without major surgical or anesthetic complications. We analyze
surgical outcome and formulate guidelines to avoid damaging the skin
and mucosa.