ENTERITIS CYSTICA PROFUNDA IN A PATIENT W ITH PEUTZ-JEGHERS SYNDROME - PSEUDOINFILTRATING LESIONS IN PATIENT WITH INTESTINAL POLYPS

We report a case of enteritis cystica profunda observed in a patient w ho, owing to both his personal and familial history, had been diagnose d ad suffering from Peutz-Jeghers syndrome. The patient was operated b ecause of a clinical picture of intestinal invagination. Together with hamartomatous polyps, anatomopathological study of the segment of the small intestine removed revealed the presence of lesions typical of E nteritis cystica profunda consisting in the presence of benign encyste d glands and pools of mucous in the deep layers of the intestinal wall . The main characteristics of this interesting and rare entity are bri efly commented.