Glomangiomas, or multiple glomus tumors, occur in disseminated, locali
zed, or congenital plaquelike forms, The first two cases of congenital
plaquelike glomangioma were described in 1990. We report a 9-year-old
girl with a congenital, violaceous, 75-cm(2) indurated plaque of the
left abdomen that showed the classic histologic findings of glomangiom
a. In our review of the world literature, we found 11 additional, well
-documented cases of glomangioma present at birth. Ten of these patien
ts had violaceous indurated plaques, and the other two had clusters of
discrete nodules. The majority of lesions were painless and enlarged
with body growth. Many patients developed satellite lesions at sites d
istant from the original glomangiomas later in life. Family history of
glomangioma was positive in 4 of the 12 patients.