Transverse vaginal septum is a defect of vertical fusion during embryo
genesis of the vagina, The estimated incidence is 1 per 30,000 to 84,0
00 women, It is infrequently associated with genitourinary tract, gast
rointestinal tract, musculoskeletal, and cardiac malformations, Previo
us reports of transverse vaginal septum have included unilateral absen
ce of the fallopian tube and ovary and absence of the proximal portion
of the fallopian tube. This report describes bilateral tubal atresia
associated with a transverse vaginal septum. A 17-year-old nulligravid
a sought medical assessment because of primary amenorrhea and cyclic p
elvic pain, Physical examination revealed a blind vaginal pouch and a
tender pelvic mass, Radiologic studies showed a transverse vaginal sep
tum 1.5 cm distal to the cervix. The septum was resected with laparosc
opic guidance, and bilateral fallopian tubal atresia was noted. The pe
lvis was otherwise normal, Patients commonly have a pelvic or abdomina
l mass, pain, and amenorrhea at time of expected menarche. Surgical re
section is the treatment of choice, Postoperative dilation may be nece
ssary to prevent restenosis. Outlook for pregnancy is encouraging desp
ite a higher than normal incidence of spontaneous abortion and endomet
riosis in such patients.