We encountered an infant with nevus sebaceus of Jadassohn who was born
with a striking pedunculated mass on the superotemporal aspect of the
anterior sclera and limbus of the left eye. In addition, two small ch
oroidal colobomas were seen in the papillomacular bundle area of the s
ame eye. Histopathologic examination of the excised mass revealed a mi
xture of ectodermal and mesodermal elements, including cartilage and b
one. These findings led to the rare diagnosis of epibulbar complex cho
ristoma.