We report 2 cases of dermatomyositis with follicular hyperkeratosis (F
HK) in children. They occurred in a 10-year-old Vietnamese girl and a
9-year-old Caucasian boy. The girl's FHK disappeared after 2 months of
treatment. The boy presented, 15 months after the onset of his dermat
omyositis, with a generalised FHK which lasted for 6 months. FHK can a
ppear before, during or after dermatomyositis. It is more often genera
lised but can be localised. Erector pili myositis and ostial hyperkera
tosis may be the explanation. The prognostic value of FHK in dermatomy
ositis is unknown. This manifestation, initially considered to be more
frequent in the Far East, is not as rare in Western countries as the
few reported cases suggest.