MALIGNANT FIBROUS HISTIOCYTOMA OF THE LUNG IN A CHILD - AN UNUSUAL NEOPLASM THAT CAN MIMIC INFLAMMATORY PSEUDOTUMOR

We describe a 12-year-old patient with a primary pulmonary mass in the left upper lung. The diagnosis of inflammatory pseudotumour was suspe cted preoperatively. After pathological examination and complete clini cal evaluation, a diagnosis of malignant primary pulmonary fibrous his tiocytoma was established. This is a very uncommon primary neoplasm of the lung and to our knoweledge only five paediatric cases have been r eported. Because of the rarity of these sarcomas and histological simi larities to benign inflammatory pseudotumour, care must be taken to av oid confusion between the two disorders particularly in intra-operativ e frozen sections. Conclusion Primary malignant fibrous histiocytoma o f the lung is an uncommon tumour that should be considered in the diff erential diagnosis of pulmonary neoplasms of childhood, The histologic al diagnosis can be difficult due to the similarities with inflammator y pseudotumour.