Background. - The blue nevus is an acquired or congenital dermal melan
osis, usually small in size. It is sometimes giant and responsible for
complications. Case report. - A newborn had a large infiltrated blue
nevus located on buttocks, lombosacral and perianal areas. He was admi
tted at the age of 3 weeks for art intestinal obstruction which was du
e to an impassable anal stenosis secondary to the infiltrated nevus. T
he tumor war excised twice, completed by plastic surgery at the age of
10 months. Conclusion. - This rare congenital giant blue nevus was re
sponsible for an unreported intestinal obstruction. The risk of malign
ant transformation was another reason for complete excision.