PARTIALLY UNROOFED CORONARY SINUS SYNDROME WITH PERSISTENT LEFT SUPERIOR VENA-CAVA, ABSENT RIGHT SUPERIOR VENA-CAVA AND RIGHT-SIDED PERICARDIAL DEFECT

Partially unroofed coronary sinus syndrome with persistent left superi or vena cava is a rare congenital anomaly. It frequently produces a ri ght-to-left shunt. We report a case in which a large left-to-right shu nt was present, because of the obstruction to left ventricular inflow as a result of the dilated coronary sinus. This abnormality was associ ated with absent right superior vena cava and a partial pericardial de fect on the right side.