Sneddon's syndrome is a systemic disease characterized by livedo retic
ularis and cerebrovascular disease. Other organs may be involved as we
ll. Typical Kidney diseases vascular lesions in the skin biopsy and/or
digital arteries biopsy can be found. Vascular diseases Arterial hype
rtension, cardiac pathology (ischemic disease, myocardial infarction,
valvulopathy), venous thrombosis and even fetal death are also found s
ometimes. We present a case of Sneddon's syndrome in which typical vas
cular lesions in the kidney were demonstrated for the first time unequ
ivocally confirming the systemic nature of this syndrome.