RADIAL CLUB HAND AND HOLT-ORAM SYNDROME

The authors describe the case of a young African girl born with a radi al club hand associated with a pedicled floating thumb, no other ortho paedic malformation was detected. A ventricular septal defect necessit ated surgery in emergency. In front of such malformative association, the Holt-Oram syndrome has been evoked. The aim of this study has been to review the etiology and classification of this rather rare malform ative association, as well as to describe the therapeutic attitudes an d surgical techniques proposed by various authors towards the radial c lub hand (1, 3, 5, 6, 7, 12).