Background: Pigmented dermatofibrosarcoma is a rare tumor of the skin
and constitutes 1-5% of all dermatofibrosarcoma. Most cases present as
polypoid multinodular growth. Occasional cases may be atrophic. We re
port an extraordinary case with progressive infraorbital atrophy. Obse
rvation: A 24-year-old woman came to us for a diffuse bluish atrophic
lesion over the left infraorbital area. The lesion progressed graduall
y over 2 years. Histologic examination revealed mature spindle cell pr
oliferation in the lower dermis and hypodermis. Interspersed were some
heavily pigmented melanocytes. Conclusion: We report an unusual case
of progressive bluish discoloration and atrophy of the infraorbital ar
ea. This is a rare manifestation of dermatofibrosarcoma.