A 16-week-old, male cocker spaniel suffering from pelvic-limb ''bunny
hopping'' as well as rigidify, spasticity, and ataxia in all limbs was
evaluated, The clinical features, electro physiological abnormalities
, and muscle histopathological and histochemical evaluations led to a
diagnosis of congenital myotonia, Myotonia is a disorder of skeletal m
uscle characterized by delayed relaxation of the muscle fiber in respo
nse to voluntary, mechanical, or electrical stimulation, The pathophys
iology of congenital myotonia remains controversial, currently propose
d pathomechanisms are discussed, To the authors' knowledge, this is th
e first case of congenital myotonia reported in a cocker spaniel.