The paper gives a brief historical survey of craniostenosis and the fi
rst operative approaches. The authors describe a classification of var
ious types of cranio-facio-stenosis and facio-cranio-stenosis and pres
ent a detailed study of their experience in this area. Operative resul
ts are discussed in function of the selected surgical procedure, the i
mmediate per- and post-operative complications and the short and long
term morbidity. The authors present their current attitude for each dy
smorphic type. They underline the heavy nature of this long-lasting an
d bleeding surgical procedure that concerns small children. They have
recorded 31 incidents in relation with surgical procedure, 10 complica
tions at short and long term, and 1 death. Such surgery requires an ex
perienced and vigilant team, associating surgeons, anesthesists and in
tensive-care physicians.