Ameloblastic carcinoma is an unusual tumour. There have been a total o
f 34 cases of ameloblastic carcinoma in the English literature to date
. Of these only 11 cases have occurred in the maxilla; The authors rep
ort the 12th such case, The histological classification for odontogeni
c carcinoma has been debated for many years and recently revised, thus
differentiating between malignant ameloblastoma and ameloblastic carc
inoma. The authors review the current literature regarding diagnosis a
nd treatment of this unusual lesion: and support the use of the: term
malignant ameloblastoma for the tumours that metastasize in spite of t
heir benign histological appearance, whereas, the ameloblastic carcino
ma is referred to as the primary tumour with malignant transformation,
regardless of its metastatic potential.