ANESTHETIC MANAGEMENT OF A PATIENT WITH HEREDITARY FRUCTOSE INTOLERANCE AND PHENYLKETONURIA

Authors
CELIKER V DURAL O ERDEM K
Citation
V. Celiker et al., ANESTHETIC MANAGEMENT OF A PATIENT WITH HEREDITARY FRUCTOSE INTOLERANCE AND PHENYLKETONURIA, Turkish Journal of Pediatrics, 35(2), 1993, pp. 127-130
Citations number
NO
Categorie Soggetti
Pediatrics
Journal title
Turkish Journal of Pediatrics → ACNP
ISSN journal
00414301
Volume
35
Issue
2
Year of publication
1993
Pages
127 - 130
Database
ISI
SICI code
0041-4301(1993)35:2<127:AMOAPW>2.0.ZU;2-B
Abstract
This is a report of a five-year-old girl with phenylketonuria (PKU) an d hereditary fructose intolerance (HFI) who underwent elective strabis mus surgery. PKU and HFI are two inborn errors of metabolism which hav e an autosomal recessive mode of inheritance. This case report describ es the anesthetic features of a patient with PKU and HFI, ''ch defect requiring specific anesthetic management.