PURPOSE: To report a 2 1/2-year-old boy who had papillary adenocarcino
ma of the ciliary body that simulated retinoblastoma. METHOD: Initiall
y treated for congenital glaucoma, the patient was referred with a whi
te mass involving the iris, chamber angle, and ciliary body. RESULTS:
Enucleation of the right eye, which was initially diagnosed as retinob
lastoma, showed a papillary adenocarcinoma of the ciliary body epithel
ium involving the posterior chamber, iris, anterior chamber, and trabe
culum. CONCLUSION: Adenocarcinoma of the ciliary body must be included
in the differential diagnosis of tumors originating from the ciliary
body in young children.