Angioid streaks of the fundus are not apparent at birth. In order to s
tudy their evolution, we examined in a retrospective manner the fundus
pictures of 111 subjects with angioid streaks. The earliest form of a
ngioid streaks became apparent at age 8 with findings of narrow short
radial discontinuous hypopigmented streaks. Thereafter angioid streaks
enlarged in length and width. The end-stage was disciform macular deg
eneration, helicoid peripapillary atrophy, or diffuse choroidal sclero
sis with obscuration of the angioid streaks. We conclude that angioid
streaks represent a dynamic manifestation of an underlying retinochoro
idal degenerative process.