ASSOCIATION OF MONOMELIC MELORHEOSTOSIS A ND SYNOVIAL CHONDROMATOSIS - A CASE-REPORT

Melorheostosis is a rare affection, of obscure etiopathologenesis, cor responding to osteosclerosis with running hyperostosis. We report the observation of melorheostosis of a lower limb occurring to an 18-year old patient who consulted for tumefaction of the lower limb with an ac hing and stiffened knee. The radiography allowed the diagnosis by show ing an aspect characterized by a running like of a candle accompanied by osteochondromatosis of the knee and the calcification of soft tissu es. The synovectomy of the knee brought about indolence and the lesion s seem to stabilise after a 3 years follow-up. The synovial osteochond romatosis seems to be an integral part of the disease. The characteris tics of melorheostosis are studied according to the data of the litera ture.