A. Adeniran et al., INCONTINENTIA-PIGMENTI (BLOCH-SULZBERGER SYNDROME) MANIFESTING AS PAINFUL PERIUNGUAL AND SUBUNGUAL TUMORS, Journal of hand surgery. British volume, 18B(5), 1993, pp. 667-669
A 25-year-old lady presented with painful periungual tumours which wer
e associated with lytic changes of underlying terminal phalanges. She
had been previously treated as a case of chronic paronychia but the pr
oblem recurred. She was subsequently diagnosed as a case of Incontinen
tia pigmenti which is a rare genodermatosis with mixed ectodermal and
mesodermal polydysplasias, onchychodystrophy being a very rare manifes
tation. She was treated by excision of painful finger lesions, but the
re is no specific treatment for the underlying condition.