INCONTINENTIA-PIGMENTI (BLOCH-SULZBERGER SYNDROME) MANIFESTING AS PAINFUL PERIUNGUAL AND SUBUNGUAL TUMORS

Authors
ADENIRAN A TOWNSEND PLG PEACHEY RDG
Citation
A. Adeniran et al., INCONTINENTIA-PIGMENTI (BLOCH-SULZBERGER SYNDROME) MANIFESTING AS PAINFUL PERIUNGUAL AND SUBUNGUAL TUMORS, Journal of hand surgery. British volume, 18B(5), 1993, pp. 667-669
Citations number
NO
Categorie Soggetti
Orthopedics,Surgery
Journal title
Journal of hand surgery. British volume → ACNP
ISSN journal
02667681
Volume
18B
Issue
5
Year of publication
1993
Pages
667 - 669
Database
ISI
SICI code
0266-7681(1993)18B:5<667:I(SMAP>2.0.ZU;2-U
Abstract
A 25-year-old lady presented with painful periungual tumours which wer e associated with lytic changes of underlying terminal phalanges. She had been previously treated as a case of chronic paronychia but the pr oblem recurred. She was subsequently diagnosed as a case of Incontinen tia pigmenti which is a rare genodermatosis with mixed ectodermal and mesodermal polydysplasias, onchychodystrophy being a very rare manifes tation. She was treated by excision of painful finger lesions, but the re is no specific treatment for the underlying condition.