Fifty-nine newborn infants with Hirschsprung's disease were treated at
the Saint-Petersburg Center of Surgery of Developmental Anomalies fro
m 1978 to 1991. The typical rectosigmoid form was found in 47.5 % and
a long zone of agangliosis in 35.6 % of children. Mortality rate - 16.
7 %. According to the development of enterocolitis, three variants of
the course of the disease in the newborns were distinguished. It is sh
own that the informativeness of the diagnostic methods increases with
the growth of the infants, and the final diagnosis of Hirschsprung's d
isease is best established at the age over two weeks on the basis of r
epeated or initially postponed contrast. study of the large intestine.
Inefficacy of nonoperative treatment conducted 2-3 days and recurrenc
e of symptoms of intestinal obstruction are indications for operative
decompression of the intestine. The performance of one-stage radical o
peration at the ige of about one month is advisable in an uncomplicate
d course of the disease.