Ac. Chang et al., EARLY BIDIRECTIONAL CAVOPULMONARY SHUNT IN YOUNG INFANTS - POSTOPERATIVE COURSE AND EARLY RESULTS, Circulation, 88(5), 1993, pp. 149-158
Background. Despite the recent wide applicability of the bidirectional
cavopulmonary shunt, there is limited reported experience in performi
ng these shunts in infants 6 months or younger. Methods and Results. B
efore October 1992, 17 consecutive infants aged 4.2 to 6.5 months (med
ian, 6.1 months) underwent bidirectional cavopulmonary shunts. The dia
gnoses were hypoplastic left heart syndrome (n=7), single right ventri
cle (n=5), and single left ventricle (n=5). All but 2 patients had pri
or palliative surgery. The bidirectional cavopulmonary shunt was perfo
rmed early on an elective basis in 9 patients; the remaining patients
had progressive cyanosis (6 patients), severe ventricular failure (1 p
atient), and coexisting restrictive bulboventricular foramen (1 patien
t). The median preoperative pulmonary arterial pressure and pulmonary
vascular resistance were 15 mm Hg and 2.3 U . m2, respectively. One pa
tient died; the overall hospital survival was 94%. The most common pos
toperative problem was transient systemic hypertension, observed in 14
(88%) of 16 survivors. Systemic arterial oxygen saturation increased
from a median of 75% before surgery to a median of 85% after surgery (
P<.05). The median hospital stay was 6 days. There were no late deaths
during follow-up (median, 12.4 months). At postoperative cardiac cath
eterization performed in 9 of 16 survivors, there was no evidence of s
evere hypoxemia, shunt narrowing, or pulmonary arteriovenous fistulas.
Of the 16 survivors, 6 have had a subsequent Fontan operation at a me
dian age of 1.9 years; there were 5 survivors. Conclusions. Early bidi
rectional cavopulmonary shunt in young infants has shown encouraging e
arly results and provides improved oxygenation with low morbidity and
mortality. We speculate that an early bidirectional cavopulmonary shun
t on an elective basis may reduce the deleterious sequelae of chronic
hypoxemia, long-term ventricular volume overload, and repeated palliat
ive procedures, thus yielding a more suitable Fontan candidate.