A patient with a tentorial dural AV fistula causing atypical trigemina
l neuralgia (TN) successfully treated by embolization is reported. The
patient developed persisting throbbing facial pain in the distributio
n of the second and third division of the right trigeminal nerve (V2,V
3) after a history of typical neuralgia for one year, preceded by a tw
o month spell of TN 6 years previously and accompanied by right-sided
pulsatile tinnitus for 10 years. The patient's mother, brother and sis
ter were also said to be affected by typical trigeminal neuralgia. A r
ight-sided dilated vein of Rosenthal due to a dural AV fistula fed by
branches of the meningeal, occipital and meningo-hypophyseal trunk of
the internal carotid artery was thought to cause trigeminal nerve comp
ression. Complete resolution of symptoms after partial intra-arterial
embolization of the main feeding arteries with N-butyroacrylate is des
cribed.