The main symptom of the congenital diaphragmatic hernia (CDH) is the r
espiratory distress due to the pulmonary hypoplasia and the persistenc
e of foetal pulmonary circulation. Sometimes the CDH appears outside o
f the neonatal period with respiratory symptoms, abdominal pain and se
ldon with intestinal obstruction. A case of CDH presenting with intrat
horacic volvulus is reported. This case shows that tendency of delayed
repair until the newborn has been recovered, require more attention b
ecause the good condition of the patient can be changed not only by th
e pulmonary hypoplasia and the persistence of the foetal pulmonary cir
culation but also by the symptoms of the intrathoracic gut complicatio
ns.