A case report and a brief review of the literature on atrial myxomas i
n young children (5 years and younger) are presented. Right atrial myx
omas are predominant in this age group in contrast to older children a
nd adults. The echocardiogram alone can provide clear anatomic informa
tion for the operation. For large left atrial myxomas, wide exposure t
hrough a transverse biatrial incision is recommended to avoid tumor ma
nipulation and facilitate en bloc resection.