From 1947 through 1992, 37 Mayo Clinic patients underwent operation fo
r the relief of tracheoesophageal obstruction that resulted from vascu
lar rings and related entities. Of the 37 patients, 18 had a double ao
rtic arch, 11 had a right aortic arch with an aberrant left subclavian
artery, 4 had a left aortic arch with an aberrant right subclavian ar
tery, 2 had a pulmonary artery sling, 1 had a right aortic arch with m
irror-image branching and a left ligamentum arteriosum, and 1 had a le
ft aortic arch, a right descending aorta, and a right ductus arteriosu
s. Symptoms consisted of stridor, recurrent respiratory infections, an
d dysphagia. The anomaly was approached through a left thoracotomy in
31 patients, through a right thoracotomy in 4, and through a median st
ernotomy in 2. Only one early postoperative death (3 %) and no late de
aths occurred. At long-term follow-up (maximal duration, 45 years), th
ree patients had residual symptomatic tracheomalacia, one of whom requ
ired right middle and lower lobectomy for recurrent pneumonia. Magneti
c resonance imaging is the imaging technique of choice for accurate de
lineation of the vascular and tracheal anatomy. When patients are symp
tomatic, vascular ring should be repaired. The surgical risk is minima
l, and the long-term results are excellent.