M. Clement et al., EPIDERMOLYSIS-BULLOSA ACQUISITA - A CASE WITH UPPER AIRWAYS OBSTRUCTION REQUIRING TRACHEOSTOMY AND RESPONDING TO CYCLOSPORINE, Clinical and experimental dermatology, 18(6), 1993, pp. 548-551
The case is reported of a 56-year-old man with epidermolysis bullosa a
cquisita (EBA) who developed such severe involvement of the upper resp
iratory tract that a tracheostomy had to be performed. Control of his
disease was ultimately obtained with cyclosporin and the use of this d
rug in EBA is reviewed.