ANTENATAL DIAGNOSIS OF TETRALOGY OF FALLOT WITH ABSENT PULMONARY VALVE ACCOMPANIED BY HYDROPS-FETALIS AND POLYHYDRAMNIOS

Citation
H. Sameshima et al., ANTENATAL DIAGNOSIS OF TETRALOGY OF FALLOT WITH ABSENT PULMONARY VALVE ACCOMPANIED BY HYDROPS-FETALIS AND POLYHYDRAMNIOS, Fetal diagnosis and therapy, 8(5), 1993, pp. 305-308
Citations number
NO
Categorie Soggetti
Obsetric & Gynecology
Journal title
ISSN journal
10153837
Volume
8
Issue
5
Year of publication
1993
Pages
305 - 308
Database
ISI
SICI code
1015-3837(1993)8:5<305:ADOTOF>2.0.ZU;2-9
Abstract
The case presented is an antenatal diagnosis of tetralogy of Fallot wi th absent pulmonary valve which was accompanied by hydrops fetalis and polyhydramnios with an absent stomach echo. Absent pulmonary valve wa s diagnosed by a cystic, pulsatile, aneurysmal dilatation of pulmonary arteries and a relatively small pulmonary valve annulus without a def inite valve echo, in which a typical to-and-fro flow pattern was detec ted by the Doppler flow analysis. We will discuss some plausible roles of the grossly enlarged pulmonary arteries on hydrops fetalis and pol yhydramnios.