H. Sameshima et al., ANTENATAL DIAGNOSIS OF TETRALOGY OF FALLOT WITH ABSENT PULMONARY VALVE ACCOMPANIED BY HYDROPS-FETALIS AND POLYHYDRAMNIOS, Fetal diagnosis and therapy, 8(5), 1993, pp. 305-308
The case presented is an antenatal diagnosis of tetralogy of Fallot wi
th absent pulmonary valve which was accompanied by hydrops fetalis and
polyhydramnios with an absent stomach echo. Absent pulmonary valve wa
s diagnosed by a cystic, pulsatile, aneurysmal dilatation of pulmonary
arteries and a relatively small pulmonary valve annulus without a def
inite valve echo, in which a typical to-and-fro flow pattern was detec
ted by the Doppler flow analysis. We will discuss some plausible roles
of the grossly enlarged pulmonary arteries on hydrops fetalis and pol
yhydramnios.