SEVERE SKIN EROSIONS AND SCALP INFECTIONS IN AEC SYNDROME

Hay-Wells syndrome is an autosomal dominant condition characterized by ankyloblepharon filiforme adnatum, ectodermal dysplasia, and cleft pa late with or without associated cleft lip (AEC syndrome). Although sev eral reported patients had eroded skin at birth and recurrent scalp in fections, these are not generally regarded as major features of the di sorder. In our experience, denuded skin at birth and chronic scalp ero sions complicated by infection are common features of this syndrome. A ggressive wound care in conjunction with early administration of topic al or systemic antibiotics is suggested.